Leukaemia: Patient Information

Leukaemia: Patient Information

General Information

Leukaemia is an umbrella term encompassing several different cancers of the blood and the blood-forming tissues of the body. All forms of leukaemia begin with problems in the creation of blood cells.

Understanding Blood Cell Creation

The body constantly produces millions of blood cells, primarily in the bone marrow—the spongy interior of bones that contains immature stem cells. In a healthy individual, these immature stem cells develop into either lymphoid or myeloid stem cells.

Lymphoid Stem Cells

Lymphoid stem cells mature into white blood cells, which are crucial components of the immune system. They first become immature cells called lymphoblasts and then mature into lymphocytes, such as B cells (producing antibodies to fight invaders) and T cells (alerting other immune cells and fighting infection directly).

Myeloid Stem Cells

Myeloid stem cells also develop into various blood cells. They become myeloblasts, which mature into monocytes and granulocytes (like neutrophils) that fight disease. Other myeloid stem cells develop into red blood cells (carrying oxygen) and platelets (aiding blood clotting).

Leukaemia develops when the DNA—the genetic instructions controlling cell activity—of a bone marrow stem cell mutates. The cell becomes cancerous, begins multiplying rapidly, and overwhelms the healthy cells in the blood and bone marrow. These diseased cells can also gather in organs such as the liver, lymph nodes, spleen, and skin.

How Leukaemia is Classified

Leukaemia is typically classified based on two main criteria:

Cell Type

By the type of stem cell that turns cancerous, either lymphoid or myeloid.

Progression Rate

As either acute or chronic.

Acute Leukaemia

Acute leukaemia affects immature cells, preventing them from developing and functioning correctly. These cells multiply rapidly, making acute leukaemia a more aggressive form of the disease.

Chronic Leukaemia

Chronic leukaemia involves mature or partially mature cells. These cells multiply more slowly and are generally less aggressive than acute leukaemia.

Types of Leukaemia

Acute Lymphocytic Leukaemia (ALL)

An aggressive form developing from immature lymphoid stem cells, affecting both adults and children.

Acute Myeloid Leukaemia (AML)

An aggressive type developing from myeloid stem cells, affecting both adults and children, though prognosis varies between groups.

Chronic Lymphocytic Leukaemia (CLL)

A slow-growing type developing from lymphoid stem cells that are further along in development. It primarily impacts older patients.

Chronic Myeloid Leukaemia (CML)

A slower-growing form developing from more mature myeloid stem cells, most often diagnosed in older adults.

B-Cell Prolymphocytic Leukaemia (B-PLL)

A rare, typically aggressive leukaemia developing from B cells that rapidly multiply.

Blastic Plasmacytoid Dendritic Cell Neoplasm (BPDCN)

An aggressive subtype of acute leukaemia, a cancer of plasmacytoid dendritic cells, most common in older patients.

Chronic Myelomonocytic Leukaemia (CMML)

A rare, slow-growing type, mainly impacting people in their 60s and older, characterised by low counts of healthy blood cells and high counts of diseased monocytes.

Hairy Cell Leukaemia

Lymphoid stem cells produce too many diseased B cells, which have thin, hair-like growths on their surface. It is typically slow to develop and more common in males aged 50 and older.

Juvenile Myelomonocytic Leukaemia (JMML)

A rare type mostly found in children aged 4 and younger, faster-growing than chronic but slower than acute leukaemia.

Large Granular Lymphocytic Leukaemia (LGLL)

A rare, generally slow-growing leukaemia developing from mature T cells or Natural Killer (NK) cells. It is primarily diagnosed in older patients.

T-Cell Prolymphocytic Leukaemia (T-PLL)

An aggressive, extremely rare form of leukaemia involving T-lymphoid stem cells. It can be slow-growing initially but often progresses to a more advanced, aggressive disease.

Symptoms of Leukaemia

Symptoms can vary, and patients with chronic leukaemia may have no symptoms at all when diagnosed. Acute forms are more aggressive and more likely to present symptoms. Many symptoms are a result of a lack of properly functioning blood cells to carry oxygen, fight infection, or clot blood.

Common leukaemia symptoms include:

  • Weakness, tiredness, and fatigue: Often caused by the leukaemia itself or low haemoglobin levels.
  • Fever and frequent infections: Due to low counts of healthy white blood cells.
  • Excessive sweating or night sweats.
  • Easy bleeding and bruising: Including gum bleeding, due to low platelet levels.
  • Recurrent nose bleeds.
  • Petechiae: A rash-like collection of tiny red spots on the skin caused by bleeding into the skin (also due to low platelet levels).
  • Shortness of breath: Can be caused by low haemoglobin levels or lung infections.
  • Swollen lymph nodes: In the neck, underarm, stomach, or groin.
  • Loss of appetite or a full feeling after eating very little food: Due to enlargement of the spleen.
  • Unexplained weight loss.
  • Bone and joint pain.
  • For female patients, longer or heavier than normal menstruation.

Diagnosis of Leukaemia

A successful treatment journey begins with an accurate and precise diagnosis. At SSCHRC, suspected leukaemia cells are examined by pathologists who specialise exclusively in diagnosing leukaemia and its many subtypes, enabling patients to receive the most effective treatment for their specific condition.

Diagnosing Leukaemia

The diagnostic process typically starts with a simple blood test called a complete blood count (CBC), which may be ordered after evaluating the patient's symptoms or as part of a routine check-up. If the CBC shows the presence of leukaemia cells or abnormal levels of red blood cells, white blood cells, or platelets, further tests are ordered for a definitive diagnosis and to determine the extent of the disease.

Common diagnostic tests include:

Biopsy

Suspected cancer cells are retrieved and studied under a microscope. For leukaemia, patients typically undergo a bone marrow biopsy, which involves taking a sample of bone marrow from the hip using a needle to check for cancerous cells.

Genetic and Molecular Testing (Molecular Profiling)

If leukaemia is diagnosed, additional testing determines whether specific chromosomes, gene mutations, proteins, or molecules are present in the diseased cells. This helps doctors determine the exact type of leukaemia and prognosis, and create a targeted treatment plan.

Lumbar Puncture (Spinal Tap)

As leukaemia may spread to the central nervous system (brain and spinal cord), a lumbar puncture is performed to examine the patient's spinal fluid for any signs of spread.

Imaging Exams

Doctors may order imaging exams to look for the presence of cancer in different parts of the body.

Leukaemia Staging

Staging is the process of learning how far a cancer has spread. While rare leukemias often do not have a set staging system, the four most common types have their own specific systems or methods to describe the disease's status, which impacts the patient's prognosis and treatment plan.

Treatment of Leukaemia

The goal of leukaemia treatment is to achieve remission (where no cancer is detectable in the patient's body) and ultimately to cure the patient. For leukaemia, complete remission means the patient's bone marrow has no detectable microscopic evidence of the disease and their blood counts have returned to normal. Patients who remain in complete remission for an extended period are considered cured, with an extremely low chance of recurrence.

At SSCHRC, internationally renowned physicians and a specialised support team collaborate daily to customise comprehensive leukaemia treatment plans. Many doctors focus on specific types of leukaemia, providing a deep level of knowledge for designing treatment plans.

Key treatment modalities include:

Chemotherapy

Drugs used to kill cancer cells, control their growth, or relieve symptoms. It may involve a single drug or a combination of drugs.

Radiation Therapy

Uses powerful beams of energy to kill cancer cells. Since leukaemia cells travel in the bloodstream, radiation is typically used when the disease has spread to the central nervous system.

Stem Cell Transplantation (Bone Marrow Transplant)

A procedure that replaces cancerous bone marrow with new, healthy bone marrow stem cells. It is usually performed after intensive chemotherapy and may be needed for patients whose leukaemia has returned, not responded to standard treatments, or who have a high-risk form of the disease.

CAR T-cell Therapy (Chimeric Antigen Receptor T cell therapy)

A treatment where T cells (a type of immune system cell) are modified to recognise and attack cancer cells.

Targeted Therapy

Drugs designed to interfere with or 'target' specific molecules (often proteins) that cancer cells need to survive, multiply, and spread.

Clinical Trials

SSCHRC offers multiple clinical trials for leukaemia, exploring new drug combinations and innovative treatments, including targeted therapies and immunotherapies, which may not be available elsewhere.

Even with normal blood counts, many leukaemia patients require ongoing maintenance therapy to remain in remission. In some cases, patients in remission may undergo a stem cell transplant to maintain remission.

Leukaemia Risk Factors

Sex

Men are more likely to develop leukaemia than women.

Age

Most types impact older adults, though some are common among paediatric patients.

Past Cancer Treatment

Prior treatment with chemotherapy or radiation therapy for a previous cancer can be a risk factor.

Family History

Having a parent, sibling, or child with certain types of leukaemia increases the risk.

Myeloproliferative Neoplasms (MPNs)

These chronic bone marrow and blood cancers (especially myelofibrosis) can transform into acute myeloid leukaemia.

Genetic Disorders

Individuals with certain genetic disorders have a higher risk, including: Ataxia telangiectasia, Bloom syndrome, Down syndrome, Fanconi anaemia, Klinefelter syndrome, Li-Fraumeni syndrome, and Wiskott-Aldrich syndrome.

Chemical Exposure

Long-term exposure to chemicals like benzene or Agent Orange.

Radiation Exposure

Exposure to radiation from nuclear incidents.

Genetic counselling may be right for you if some cases of leukaemia have been passed down from one generation to the next.

Sri Shankara Cancer Hospital Footer Shankara Cancer Hospital & Research Center